Results
Significantly fewer women with Marfan syndrome gave birth, compared to the background population. In Marfan syndrome, complications related to cervix were increased (HR: 19.8 (95% CI: 2.2-177.5)) and the number of caesarean sections was higher (HR: 2.09 (95% CI: 1.41-3.08)). No women with known Marfan syndrome had a pregnancy related aortic dissection and the consequences of pregnancy and delivery on future aortic events seemed limited. Among undiagnosed women with Marfan syndrome there were more foetal deaths and all delivery-related dissections came from this subgroup.