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FIGURES:Figure 1: Multiple cystically dilated intra hepatic biliary ducts in
segments V, VI, VII and VIII of the liver. These ducts show no
enhancement in post contrast images with central enhancing portal
radicle giving central dot sign (arrow). However, common bile duct is
normal.
Figure 2: Ducts show no enhancement in post contrast images with central
enhancing portal radicle giving central dot sign (arrow).
Figure 3: Multiple cystically dilated intra hepatic biliary ducts
(arrow).
Figure 4: CT Scan (Coronal view) Multiple variable sized cystic lesions
are seen (arrows) involving all poles of both kidneys. No calcification,
septation or enhancing solid components seen within the cyst.
Consent: Written informed consent was taken from the patient’s
parents before writing the manuscript.