Introduction
Dystrophinopathies in the form of Duchenne and Becker’s muscular dystrophies affect 1:5000 newborn males worldwide1. As patients age, myocyte degeneration and myocyte fibrosis occur, resulting in progressive immobility and respiratory failure. While neuromuscular disease is severe in Duchenne Muscular Dystropy (DMD) and milder in Becker’s Muscular Dystrophy (BMD), dystrophin deficient cardiomyopathy tends to be more unpredictable in onset. Myocardial fibrosis and arrhythmic manifestations are common and do not necessarily correlate to the degree of skeletal muscle involvement2. In fact, in cases of more mild muscular disease, cardiac dysfunction may precede symptomatic skeletal muscle involvement3. Periodic cardiac evaluation including imaging and routine surveillance of cardiac arrhythmias is recommended, and advanced imaging frequently detects myocardial fibrosis under the age of ten years old4.