INTRODUCTION
BAV is the most common congenital anomaly of the heart with a prevalence that ranges from 0.5% to 2%. (1-3) Its association with other congenital cardiac anomalies is well established and associated anomalies are often the cause of early disease diagnosis during childhood.(4) But when BAV is isolated, it has minimal progression during childhood (5) and usually presents later in life with either valvulopathy or aortopathy. The valvulopathy associated with BAV can present itself as insufficiency, stenosis or a mixed disease.(6, 7) Severity of valvulopathy varies between mild and non-significant to moderate or severe valve dysfunction.(3, 8) The associated aortopathy is variable in terms of the size of the aorta and it’s a atomic location. Patients with BAV might have normal sized aorta or aneurysm/ectasia of the aortic root, ascending aorta, or both.(9, 10) The aim of this study was to assess the reported prevalence of BAV in a large Echocardiography (ECHO) database and to better understand the presentation of BAV in different age groups, the risk factors for thoracic aortic aneurysms and the surgical intervention stratified to each age group.