Complete transposition of the great arteries is incompatible with life
without corrective surgery in the neonatal period. Even in the presence
of large intracardiac shunts, a case of un-operated d-TGA that survived
to late adulthood is thought-provoking. We described a case of
un-operated d-TGA presenting at 46 years of age who had large secundum
type ASD, pulmonary hypertension, pulmonary artery aneurysm, situs
inversus, mirror image dextrocardia and abnormal origin of the coronary
artery. The management of an un-operated case of d-TGA surviving to late
adulthood has made it important to share case-based experiences as there
are no evidence-based data.