INTRODUCTION:
The word teratoma is derived from the Greek word ’teratos,’ which means
a monster. The most common benign lesion in young women is a mature
cystic teratoma. Malignant transformation is rare and seen in less than
3% of the cases [1]. The chances of malignant transformation
increase with age and are most common in post-menopausal women of the
4th to 5th decade [2]. Mature cystic teratoma of the ovary (MCTO)
can transform into squamous cell carcinoma, adenocarcinoma, and
papillary carcinoma, squamous cell carcinoma being the most common.
Previous studies have shown a poor prognosis for the malignant
transformation of MCTO [3]. It is nearly impossible to diagnose the
malignant transformation of MCTO preoperatively due to the tumor’s
rarity and its similarity to MCTO [4].
Furthermore, due to the condition’s rarity, no standard treatment has
been established for its management yet. There are several studies of
malignant transformation of MCTO; however, undifferentiated carcinoma
arising in the MCTO is exceedingly rare. Here, we present a rare case of
undifferentiated carcinoma arising from MCTO.