Introduction:
Fifteen percent of sarcomas are located in the retroperitoneal space[1] . Liposarcoma is a rare malignant tumor that originates from primitive mesenchymal cells rather than from mature adipose tissue. It is the most common subtype of retroperitoneal sarcomas[2] .
Retroperitoneal liposarcoma (RLS) may reach a very large size and may cause tumoral infiltration of adjacent organs and large vessels before being diagnosed. The average diameter of the tumor is 20 – 25 cm with an average weight of 15 to 20 Kg. The complete resection of the mass and a favorable histopathologic grade are positively associated with long-term disease-free survival [2]. However, preserving neighboring structures, in particular the kidney, is actually non-consensual and still challenging. Thus, nephrectomy should be discussed case by case.
We report herein a case of a 68-year-old female with a giant retroperitoneal liposarcoma arising from the right perirenal space.