1 | INTRODUCTION
Wilms tumor, also referred to as nephroblastoma, accounts for
~90% of all pediatric renal
malignancies[1]. However, extrarenal Wilms tumor
(ERWT) manifestation remains rare, occurring in approximately 3% of all
Wilms tumor cases[2]. Such extrarenal tumors
typically present in the form of an asymptomatic mass within the
abdomen, although they can be accompanied by abdominal pain, hematuria,
and/or hypertension, with each occurring in roughly a quarter of such
cases[3]. Dilated cardiomyopathy and congestive
heart failure (CHF) are rare presentations for such tumors, with only a
few previously reported cases exhibiting these symptoms. There have not
been any published reports to date of a case of ERWT presenting with
hypertension, dilated cardiomyopathy, and CHF. Here we present the first
case of ERWT with these rare symptoms and review the relevant
literature.