Introduction
Paraneoplastic neurologic syndromes (PNS) are rare in pediatrics and are reported in only a few pediatric malignancies like Hodgkin lymphoma, neuroblastoma and teratoma (1). Opsoclonus-myoclonus, encephalitis, cerebellar syndrome and encephalomyelitis are some of the reported paraneoplastic neurological syndromes. Paraneoplastic encephalitis is usually associated with neuroendocrine tumors and lymphomas (2). We report a case of possible paraneoplastic encephalitis in a patient of adrenocortical carcinoma (ACC).