Introduction
Paraneoplastic neurologic
syndromes (PNS) are rare in pediatrics and are reported in only a few
pediatric malignancies like Hodgkin lymphoma, neuroblastoma and teratoma
(1). Opsoclonus-myoclonus, encephalitis, cerebellar syndrome and
encephalomyelitis are some of the reported paraneoplastic neurological
syndromes. Paraneoplastic encephalitis is usually associated with
neuroendocrine tumors and lymphomas (2). We report a case of possible
paraneoplastic encephalitis in a patient of adrenocortical carcinoma
(ACC).