Abstract
Succinate dehydrogenase-deficient renal cell carcinoma (SDH-deficient RCC) is a malignant tumor associated with the loss of a mitochondrial enzyme. Owing to its rarity and limited imaging, SDH-deficient RCC is always misdiagnosed or escapes diagnosis. Here, we report a case of SDH-deficient RCC in a 50-year-old male characterized by multimodal images and confirmed by pathological examination.